Clinical Food Study to Evaluate the Effect of KB195 on Gut Nitrogen Metabolism in Patients With Urea Cycle Disorders

Inclusion Criteria: * Confirmed UCD patient at any age ≥ 14 years * Parental/legal guardian permission or patient's written informed consent or assent, as applicable * Be willing and able to comply with study requirements Exclusion Criteria: * Any medical condition unrelated to the sequelae of UCD * Patient has N-acetylglutamate synthase (NAGS) deficiency * Recent hospitalization or risk for metabolic decompensation * Liver transplantation * Systemic antibiotics, probiotics or prebiotics that do not align with study guidances * Change in dose or frequency of any drug or other compound to modulate GI motility * Contraindications or known allergy/sensitivity to the use of the study products * Use of an investigational drug, product or device within 30 days prior to Screening Visit, or current enrolment in another investigational drug, product, or device study * Considered to be at risk for noncompliance or unlikely for any reason to be able to comply with the study procedures