Effect of Game Based Approach on Oxygenation, Functional Capacity and Quality of Life in Primary Ciliary Dyskinesia

Hacettepe University32 enrolled

Overview

Impaired pulmonary function, decreased physical activity, functional capacity and depending on these factors are reported in patients with primary ciliary dyskinesia in recent studies. The purpose of this study to evaluate the effects of game based approach on pulmonary function, functional capacity and quality of life in patients with primary ciliary dykinesia.

Primary ciliary dyskinesia (PCD) is an autosomal recessive hereditary disorder characterized by congenital structural abnormalities and impairment of respiratory function. Mucociliary clearance is affected by disorders in the structure and movement of cilia. That causes repeated infections in the upper and lower respiratory tract.In addition to mucociliary effects and impaired lung function, it is thought that there may be a decrease in respiratory muscle strength and functional capacity. One of the factors affecting functional capacity is the level of physical activity. For these reasons, the management of the respiratory system in patients with PCD is very important. In addition to airway clearence techniques, approaches to increase physical activity are also important. It was thought that severe physical activity could be an important determinant of cardiopulmonary functional capacity in patients with mild to moderate PCD. The level of physical activity is known to be associated with quality of life. In literature no study investigated the effects of game based approach on oxygenation, functional capacity and quality of life in patients with PCD. Game based approach is a new method lead to increase physical activity. In literature there is no study investigated the effects of game based approach on oxygenation, functional capacity and quality of life in patients with PCD.

Study Type

INTERVENTIONAL

Allocation

RANDOMIZED

Purpose

TREATMENT

Masking

SINGLE

Enrollment

Conditions

Primary Ciliary Dyskinesia Kartagener Syndrome Immotile Cilia Syndrome

Interventions

Home based therapyOTHER

Airway clearence techniques

Game and home based therapyOTHER

Game based approach programme and airway clearence techniques

Eligibility

Sex: ALLMin age: 6 YearsMax age: 18 Years

Medical Language ↔ Plain English

Inclusion Criteria: * Being diagnosed with PCD * Being clinically stable * Between 6-18 years old * Volunteer to participate in research Exclusion Criteria: * Not having a stable clinical condition * Patients with severe neuromuscular, musculoskeletal and rheumatological problems * Patients with loss of balance * Not being cooperative

Locations (1)

Hacettepe University, Faculty of Health Sciences, Department of Physiotherapy and Rehabilitation

Ankara, Turkey (Türkiye)

Outcomes

Primary Outcomes

Functional capacity using six minute walk test

Six minute walk test will be performed in a long, straight, enclosed corridor 30 meters in length. Patients are required to walk in their walking speed with standardized instructions.

Time frame: Change from baseline distance of six minute walk test in 8 weeks

Distance of six minute walk test

The distance walked will be recorded as meters at the end of 6 minute walk test.

Time frame: Change from baseline distance of six minute walk test in 8 weeks