Data from patients with the orphan disease of lymphangioleiomyomatosis (LAM) which performed a pulmonary Rehabilitation program will be analyzed retrospectively. Data will be taken from the internal data base of the reference Center (Schoen Klinik Berchtesgadener Land, Schoenau, Germany) where These data were collected during clinical routine. Data will be included from the year 2000 until now. A retrospectively matched COPD cohort will be included for comparison.
Study Type
OBSERVATIONAL
Enrollment
58
Patients will perform a comprehensive, inpatient pulmonary rehabilitation program for 4 weeks duration
Schoen Klinik Berchtesgadener Land
Schönau am Königssee, Germany
Change from baseline 6 Minute walk distance at week 4
the walked distance in meter will be the Primary outcome of the 6 Minute walk test
Time frame: baseline and week 4
Change from baseline Quality of life at week 4
the physical and mental health component summary score from the Short Form 36 Health Questionnaire will be recorded. Score range from 0 to 100 with lower scores indicating worse impairment
Time frame: baseline and week 4
Change from baseline lung function at week 4
forced expiratory volume in 1 second and inspiratory vital capacity will be provided in Liter and percent predicted
Time frame: baseline and week 4
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