Hereditary Epidermolysis Bullosa (EBH) are rare dermatologic diseases characterized by cutaneous and mucosa fragility. Oral manifestations of few small cohort have been published. The main objective of this multicentric cohort study first in Europe was to report the oral status of these patients that were consulted in the MRDRC of this disease in Nice (France), Toulouse (France) and Louvain (Belgium). Then a correlation between the oral characteristics and the EBH type will be made, in order to facilitate the management of patient care and the prevention program that can be established to improve their oral health.
Study Type
OBSERVATIONAL
Enrollment
41
clinical oral examination
Nice Hospital
Nice, France
Toulouse University
Toucy, France
Dental structural abnormalities and/or caries
number of defect /dental caries dor each toth
Time frame: 1 day
gingival biotype
clinical observation of gingiva (thin or thick)
Time frame: 1 day
gingival status
observation and classification of the gingiva (healthy, inflammed or hyperplastic)
Time frame: 1 day
plaque and gingival index
registration of plaque and gingival index according to the Loë and Silness method
Time frame: 1 day
oral lesion
number and localisation of the blister/scars/flanges scars on a sketch of a mouth
Time frame: 1 day
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