Primary immunodeficiencies represent a underdiagnosed group of rare diseases which if diagnosed well and in time can be treated in an efficient manner and prevent complications that may affect the quality of patients life in an severe manner. Neither in Costa Rica nor in Central America studies or national registries regarding the prevalence and characterization of primary immunodeficiencies in adult patients exist up to now. This study reflects for the first time the epidemiologic situation of primary immunodeficiencies in a Central American country, characterizing adult patients diagnosed with primary and idiopathic immune disorders treated in two specialized immunodeficiency clinics in Costa Rica.
Study Type
OBSERVATIONAL
Enrollment
137
Hospital Calderon Guardia
San José, Costa Rica
Clinical manifestations of all adult patients diagnosed with primary and idiopathic immune defects
Describe the clinical manifestations of all adult patients diagnosed with primary and idiopathic immune defects attended in the primary immunodeficiency clinics of the Hospitals Mexico and Dr. Rafael Ángel Calderón Guardia during the study period.
Time frame: 1 year
characterization of immunodeficient patients
Characterize immunodeficient patients using sociodemographic and health variables.
Time frame: 1 year
Concordances between clinical manifestations and literature
•Establish concordances between the clinical manifestations of the group of patients under study with those described in the literature according to the different pathologies.
Time frame: 1 year
organic complications
Record organic complications secondary to immunodeficiency status.
Time frame: 1 year
type and degree of immunodeficiency
Differentiate the type and degree of immunodeficiency of each patient.
Time frame: 1 year
pathonges that cause infectious
Report isolated pathogens that cause infectious manifestations in patients.
Time frame: 1 year
bacteria present in upper airways
•Report the colonizing bacteria present in the cultures of the upper airways of the patients requested in the initial approach.
Time frame: 1 year
This platform is for informational purposes only and does not constitute medical advice. Always consult a qualified healthcare professional.